První zkušenosti jednoho centra s použitím přípravku Octaplas® v léčbě pacientky s vrozenou formou trombotické trombocytopenické purpury
Authors:
Z. Čermáková 1; Š. Blahutová 2; M. Kořístka 2; R. Hrdličková 2
Authors‘ workplace:
Lékařská fakulta Ostravské univerzity
1; Krevní centrum Fakultní nemocnice Ostrava
2
Published in:
Transfuze Hematol. dnes,18, 2012, No. 4, p. 162-164.
Category:
Comprehensive Reports, Original Papers, Case Reports
Overview
Congenital form of TTP (Upshaw-Schulman syndrome) is a severe, life-threatening disease in which plasma remains the first-choice treatment. Patients are dependent on regular therapeutic plasma exchange or plasma infusion. A plasma volume of 1-1.5 is usually substituted by donors’ quarantine plasma. In these patients, secondary mild/severe side effects (allergic reactions, transfusion-induced acute lung injury) are very often observed. The authors comment on their first experience with the use of Octaplas® (Octapharma, Vienna, Austria).
Key words:
thrombotic thrombocytopenic purpura, Octaplas, therapeutical plasma exchange
Sources
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Labels
Haematology Internal medicine Clinical oncologyArticle was published in
Transfusion and Haematology Today
2012 Issue 4
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