Dissecting Aortic Aneurysm at Marfan Syndrome – Case Report
Authors:
P. Šantavý; M. Čermák; R. Hájek; K. Fábiková; J. Novotný *; P. Němec
Authors‘ workplace:
Kardiochirurgická klinika FN Olomouc, přednosta doc. MUDr. Petr Němec, CSc.
; Radiodiagnostické oddělení, Vojenská nemocnice Olomouc
*
Published in:
Rozhl. Chir., 2007, roč. 86, č. 7, s. 359-362.
Category:
Monothematic special - Original
Overview
The authors present the case report of a Marfan syndrome patient with aneurysm of ascending, dissecting aneurysm of descending and abdominal aorta. Ascending aorta replacement with aortic valve sparing procedure was performed at first surgery. Later on descending and abdominal aorta were replaced. The patient was reoperated because of a chylus collection in retroperitoneal space. Three months following surgery the patient is completely recovered.
Key words:
dissecting aortic aneurysm – Marfan syndrome
Sources
1. Kainulainen, K., Pulkkinen, L., Savolainen, A., Kaitila, I., Peltonen, L. Location on chromosome 15 of the gene defect causing Marfan syndrome. N. Engl. J. Med., 1990; 323: 935–939.
2. Gott, V. L., Laschinger, J. C., Cameron, D. E., Greene, P. S., Gillinov, A. M., Alejo, D. E., Fleischer, K. J., Dietz, H. C., Pyeritz, R. E., Anhalt, G. J., et al. The Marfan syndrome and the cardiovascular surgeon. European Journal of Cardio-Thoracic Surgery, vol. 10, Issue 3, 1996, p. 149–158.
3. David, T. E., Feindel, C. M. An aortic valve sparing operation for patients with aortic incompetence and aneurysm of the ascending aorta. J. Thorac. Cardiovasc. Surg., 1992; 103: 617–622.
4. Bentall, H., De Bono, A. A technique for complete replacement of the ascending aorta. Thorax, 1968, Jul; 23(4): 338–339.
5. Hopkins, R. A. Aortic valve leaflet sparing and salvage surgery: evolution of techniques for aortic root reconstruction. European Journal of Cardio-Thoracic Surgery, vol. 24, Issue 6, December 2003, p. 886–897.
6. Bachet, J., Guilmet, D., Cron, C., Dreyfus, G., Goudot, B., Piquois, A., Brodaty, D., Dubois, C., de Lentdecker, P., Rosier, J. Protection of the spinal cord during surgery of thoraco-abdominal aortic aneurysms. European Journal of Cardio-Thoracic Surgery, vol. 10, Issue 10, 1996, p. 817–825.
7. Coselli, J. S., LeMaire, S. A. Current status of thoracoabdominal aortic aneurysm repair in Marfan syndrome. J. Card. Surg., 1997; 12: 167–172.
8. Ince, H., Rehders, T. C., Petzsch, M., Kische, S., Nienaber, C. A. Stent-grafts in patients with Marfan syndrome: J. Endovasc. Ther., 2005; 12 (1), 82–88.
Labels
Surgery Orthopaedics Trauma surgeryArticle was published in
Perspectives in Surgery
2007 Issue 7
Most read in this issue
- The “Pancreatic Unit“ in the Treatment of Severe Necrotizing Pancreatitis
- Diagnosing Occult Pertrochanteric Fractures of Proximal Femur with MRI
- Surgical Management of Intrahepatic Cholelithiasis – Two Case Reviews
- Stoma Procedures in the Cogenital Digestive Tract Malformations