Adults with congenital heart diseases

Czech version

Authors: J. Rubáčková-Popelová
Authors‘ workplace: Centrum pro dospělé s vrozenou srdeční vadou, Kardiochirurgické oddělení, Nemocnice Na Homolce, Praha
Published in: Kardiol Rev Int Med 2015, 17(4): 315-321
Category: Cardiology Review

Overview

The number of adults with congenital heart diseases (CHD) has recently been estimated at 2,800–3,000 per one million inhabitants and has been constantly increasing. Approximately one half of the adults with CHD suffer from complex lesions requiring follow-up in specialised centres where there is sufficient knowledge of CHD among general cardiologists, internists and general practitioners. Many adults treated for CHD in childhood require further surgery or interventions in adulthood, preferably in a specialised centre. According to the guidelines, such interventions may be indicated even in asymptomatic or less symptomatic patients. Patients who undergo such interventions after developing significant symptoms have a worse prognosis and worse long-term postoperative results. The Centre for Adults with CHD in the Na Homolce Hospital in Prague has operated on more than 840 adults with CHD since 2005. The 30-day operative mortality is 1.3%. Complex and rare CDH accounts for 43% of all surgeries. Reoperations after previous surgery in childhood represents 44% of all cases. Good results can be attributed to the expertise and good co-operation of a team trained in adult CHD, including adult and paediatric cardiac surgeons, cardio-anaesthesiologists and cardiologists.

Keywords:
adult congenital heart diseases – surgery – residual findings

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