The Peutz-Jeghers Syndrom – A Case Review
Authors:
M. Škrovina 1; S. Czudek 1; J. Bartoš 1; I. Ferák 2; L. Adamčík 1; E. Bezunková 3; R. Vaňko 1
Authors‘ workplace:
Chirurgické oddělení, Onkocentrum J. G. Mendela a Nemocnice Nový Jičín
primář: MUDr. S. Czudek, CSc.
1; Patologie, P & R LAB s. r. o., Onkocentrum J. G. Mendela Nový Jičín, primář: MUDr. I. Ferák, Ph. D.
2; Radiodiagnostické oddělení, Onkocentrum J. G. Mendela a Nemocnice Nový Jičín
primář: MUDr. M. Velkoborský
3
Published in:
Rozhl. Chir., 2007, roč. 86, č. 1, s. 24-26.
Category:
Monothematic special - Original
Overview
Introduction:
The authors present a case review of a localized Peutz-Jeghers syndrome of the caecum, emulating a carcinoma.
Methods:
The patient who presented with insignificant family history with a diagnosed stenosing tumor of his appendix and histological findings of highly suspected adenocarcinoma, was indicated for surgical revision and right-sided hemicolectomy.
Results:
The patient underwent laparoscopically assissted right-sided hemicolectomy and his postoperative course was adequate. The final histological finding diagnosed solitary hamartoma of the Peutz-Jeghers polyp.
Conclusion:
Differential diagnostic reasoning in patients with negative family history and unclear case history with findings of polypous tumorous lesions of the GIT, should also consider the Peutz-Jeghers syndrome. The syndrome is related to a high risk of malignancies in the elderly.
Key words:
Peutz-Jeghers syndrome – caecum – laparoscopic resection
Sources
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Perspectives in Surgery
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