Two rare symptomatic vascular anomalies in one child

Czech version

Authors: Murgašová Michaela ^1,2*; Ová Krá Terézia ¹; Zeleňák Kamil ³; Bánovčin Peter ¹
Authors‘ workplace: Klinika detí a dorastu, Jesseniova lekárska fakulta, v Martine, Univerzita Komenského, v Bratislave, Univerzitná, nemocnica Martin, Martin, Slovenská republika ¹; Ambulancia pediatrickej, hematológie a onkológie, Univerzitná nemocnica Martin, Martin, Slovenská republika ²; Rádiologická klinika, Jesseniova, lekárska fakulta v Martine, Univerzita Komenského, v Bratislave, Univerzitná nemocnica Martin, Martin, Slovenská republika ³
Published in: Čes-slov Pediat 2024; 79 (6): 329-334.
Category: Case Report
doi: https://doi.org/10.55095/CSPediatrie2024/058

Overview

The spectrum of vascular anomalies with different biological behavior is very wide. They are divided into vascular malformations and vascular tumors – hemangiomas. Although many of them look similar, their clinical manifestation is different – from a mild self-limiting course to life-threatening complications requiring an intensive multidisciplinary therapeutic approach. Frequently, even in professional practice, all vascular anomalies are incorrectly called hemangiomas. It is very important to classify and name the vascular anomaly correctly so that we can choose the right treatment and prevent serious complications. Infantile hemangioma (IH) is the most common vascular tumor in children. It is a lesion with a completely typical biological behavior and a well-taken history is usually sufficient to distinguish it from other vascular anomalies. Only a small part of IH represents a risk to the child and requires systemic or combined multimodal treatment. Vascular malformations represent a heterogeneous group of usually developmental abnormalities of the vascular system and can affect any type of vessels. These are often mixed vascular lesions. Symptomatic vascular malformations are rare in children and often are diagnostic and therapeutic challenge for doctors. We present a case report of a non-syndromic patient with two rare symptomatic vascular anomalies requiring multidisciplinary care.

Keywords:

childhood – infantile hemangioma – carotid-cavernous fistula – vascular anomalies – beta blocker – endo-vascular treatment

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