Rare causes of pulmonary hypertension in infants

Czech version

Authors: Genzor Martin; Kováčiková Ubica; Škrak Peter
Authors‘ workplace: Oddelenie anestéziológie a intenzívnej medicíny, Detské kardiocentrum, NUSCH a. s., Bratislava, Slovenská republika
Published in: Čes-slov Pediat 2024; 79 (6): 323-328.
Category: Case Report
doi: https://doi.org/10.55095/CSPediatrie2024/039

Overview

Pulmonary hypertension is a serious disease leading to right-sided heart failure. Although the incidence of pulmonary hypertension associated with congenital heart diseases is decreasing, the incidence of pulmonary hypertension associated with other non-cardiac diseases has an increasing trend. We provide three case reports of patients with noncardiac causes of pulmonary hypertension who were hospitalized in the Pediatric Cardiac Center, a newborn with tricuspid valve dysplasia and thyreotoxicosis, a newborn with congenital pulmonary lymphangiectasis treated with extracorporeal oxygenation, and an infant with alveolar capillary dysplasia with misalignment of pulmonary veins. Pulmonary hypertension is diagnosed based on echocardiography followed by a detailed differential diagnostic workup. In addition to the symptomatic treatment of pulmonary hypertension, patient management also focuses on the treatment of underlying diseases.

Keywords:

Pulmonary hypertension – neonatal thyrotoxicosis – alveolar capillary dysplasia – congenital pulmonary lymphangiectasia

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