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Overview of histiocytic and dendritic disorders by the 5th version of WHO Classifi cation of Hematolymphoid Tumours from 2022


Authors: Z. Adam 1;  M. Hermanová 2;  T. Horváth 3;  L. Pour 1;  S. Ševčíková 4;  K. Starý 5;  M. Dastych 5;  Z. Řehák 6;  Z. Adamová 7,8;  Z. Král 1
Authors‘ workplace: Interní hematologická a onkologická klinika LF MU a FN Brno 1;  I. ústav patologie, LF MU a FN u sv. Anny v Brně 2;  Chirurgická klinika LF MU a FN Brno 3;  Ústav patologické fyziologie, LF MU Brno 4;  Interní gastroenterologická klinika LF MU a FN Brno 5;  Oddělení nukleární medicíny, MOU Brno 6;  Chirurgické oddělení, Nemocnice ve Frýdku-Místku 7;  Chirurgické oddělení, Vsetínská nemocnice 8
Published in: Klin Onkol 2024; 38(3): 164-177
Category: Reviews
doi: https://doi.org/10.48095/ccko2024164

Overview

Background: Histiocytoses are rare disorders characterized by the accumulation of macrophages, dendritic cells, or monocyte-derived cells in various tissues and organs of children and adults, with a wide range of clinical manifestations, presentations, and histology. The histiocytoses are classified according to the WHO Classification, the last version of which was published in 2022, or according to the Histiocyte Society Classification, with the last version published in 2016. Purpose: This text provides an overview of histiocytoses as described in the WHO Classification 2022.

Keywords:

5th version of WHO Classification of histiocytic and dendritic neoplasms – Histiocyte Society classification of histiocytic disorders


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