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Consensual guidelines of the Czech National Haemophilia Programme (CNHP) for the diagnosis and treatment of patients with haemophilia, 3rd edition, year 2021


Authors: Pracovní Skupina Čnhp Pro Standardy:;  P. Smejkal 1;  J. Blatný 2;  Z. Hajšmanová 3;  A. Hluší 4;  R. Hrdličková 5;  E. Zápotocká 6;  M. Penka 1;  Rady Koordinační Jménem;  Výkonné Rady Čnhp:;  B. Blažek 7;  Z. Čermáková 5;  Z. Černá 8;  P. Ďulíček 9;  J. Hak 10;  V. Komrska 6;  P. Ovesná 11;  D. Pospíšilová 12;  D. Procházková 13;  P. Timr 14;  J. Ullrychová 15;  I. Vonke 16;  L. Walterová 17
Authors‘ workplace: Oddělení klinické hematologie, FN Brno 1;  Oddělení dětské hematologie, FN Brno 2;  Ústav klinické bio chemie a hematologie, FN Plzeň 3;  Hemato-onkologická klinika, FN Olomouc 4;  Klinika hematoonkologie a Krevní centrum, FN Ostrava 5;  Klinika dětské hematologie a onkologie, FN Motol, Praha 6;  Klinika dětského lékařství, FN Ostrava 7;  Dětská klinika, FN Plzeň 8;  IV. interní hematologická klinika, FN Hradec Králové 9;  Dětská klinika, FN Hradec Králové 10;  Institut bio statistiky a analýz LF MU, Brno 11;  Dětská klinika, FN Olomouc 12;  Dětská klinika, Krajská zdravotní a. s., Masarykova nemocnice v Ústí nad Labem 13;  Dětské oddělení, Nemocnice České Budějovice 14;  Oddělení klinické hematologie, Krajská zdravotní a. s., Masarykova nemocnice v Ústí nad Labem 15;  Oddělení klinické hematologie, Nemocnice České Budějovice 16;  Oddělení klinické hematologie, Krajská nemocnice Liberec 17
Published in: Transfuze Hematol. dnes,27, 2021, No. 1, p. 73-90.
Category: Best Practices
doi: https://doi.org/10.48095/cctahd202173

Overview

The aim of these guidelines is to set-up and standardize dia­gnostic as well as therapeutic approaches to patients with haemophilia according to updated scientific evidence. Update of the original consensual guidelines reflects new available data plus advent of new drugs and recommends the optimal dosage for treatment. The system for haemophilia care in Czech Republic is briefly described.

Keywords:

haemophilia – guidelines – dia­gnosis – treatment – Prophylaxis


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