Acute aortic dissection in pregnant women with Marfan syndrome

Czech version

Authors: T. Dierzé; F. Toušek; Š. Šindelářová; A. Mokráček
Authors‘ workplace: Primář: MUDr. František Toušek, FESC. ; Kardiocentrum – kardiologie, Nemocnice České Budějovice, a. s.
Published in: Prakt. Lék. 2010; 90(2): 97-101
Category: Case Report

Overview

Marfan syndrome is an inheritable connective tissue disorder. Pregnant women with Marfan syndrome are at risk of cardiovascular events, one of which is the life threatening acute aortic dissection. That is why it is important to diagnose a dilatation of aortic root in time, preferably before conception, and to propose the optimal treatment since dilatation of aortic root mostly anticipates the aortic dissection. Treatment strategy includes pharmacotherapy and cardiosurgical reconstruction of aorta and eventually aortic valve replacement. The cooperation of cardiologists, cardiosurgeons, gynecologists, anaesthesiologists and pediatricians is necessary to ensure a safe pregnancy, delivery and puerperium of women with Marfan syndrome.

Key words:
Marfan syndrome, pregnancy, aortic aneuryzm, acute aortic dissection, aortic valve replacement, aortic root replacement.

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