Chronická disekujúca aneuryzma vzostupnej časti aorty s rozsiahlym intramurálnym trombom a izolovanými defektami v stene aorty

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Autoři: Silvia Farkašová Iannaccone ¹; Dorota Sopková ¹; Marián Švajdler jr. ²; Daniel Farkaš ³; Lucia Mistríková ⁴; Roman Mezencev ⁵
Působiště autorů: Department of Forensic Medicine, Faculty of Medicine, Pavol Jozef Šafárik University, Košice, Slovak Republic ¹; Šikl’s Department of Pathology, Charles University, Medical Faculty Hospital, Pilsen, Czech Republic ²; Medico-Legal and Pathological-Anatomical Department of Health Care Surveillance Authority, Košice, Slovak Republic ³; Department of Heart Surgery, East Slovak Institute for Cardiovascular Diseases, Košice, Slovak Republic ⁴; School of Biological Sciences, Georgia Institute of Technology, Atlanta, GA, USA ⁵
Vyšlo v časopise: Čes.-slov. Patol., 55, 2019, No. 2, p. 115-119
Kategorie: Původní práce

Souhrn

V popisovanom prípade autori dokumentujú makroskopický a mikroskopický pitevný nález chronickej disekujúcej aneuryzmy vzostupnej časti aorty a aortálneho oblúka s izolovanými trhlinami v stene aorty bez jej prasknutia u 71-ročnej ženy s minimálnou klinickou symtomatológiou. Aneuryzmatické rozšírenie priesvitu aorty bolo podmienené nielen vyklenutím cievnej steny na základe prítomnosti organizovaného intramurálneho trombu, ale aj v dôsledku prítomnosti plošného defektu intimy a medie aorty so zachovaním celistvosti obvodu fibroticky zmenenou adventíciou. Histologicky bola v torakálnej aorte zistená cystická degenerácia medie s minimálnymi prejavmi aterosklerózy.

Klíčová slova:

disekujúca aneuryzma aorty – disekcia aorty – intramurálny trombus aorty – degenerácia medie – akumulácia mukoidnej extracelulárnej hmoty

Zdroje

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