Vein of Galen congenital malformation in newborn
Authors:
H. Kolarovszká 1; L. Časnocha Lúčanová 1; K. Zeleňák 3; R. Richterová 2; M. Kozár 1; K. Maťašová 1
Authors‘ workplace:
Neonatologická klinika, Jesseniova lekárska fakulta v Martine, Univerzita Komenského v Bratislave
Univerzitná nemocnica Martin
prednosta prof. MUDr. M. Zibolen, CSc.
1; Neurochirurgická klinika, Jesseniova lekárska fakulta v Martine, Univerzita Komenského
v Bratislave, Univerzitná nemocnica Martin
prednosta doc. MUDr. B. Kolarovszki, PhD.
2; Rádiologická klinika, Jesseniova lekárska fakulta v Martine, Univerzita Komenského v Bratislave
Univerzitná nemocnica Martin
prednosta doc. MUDr. K. Zeleňák, PhD.
3
Published in:
Čes-slov Pediat 2016; 71 (5-6): 275-280.
Category:
Case Report
Overview
Vein of Galen aneurysmal malformation is rare vascular developmental anomaly that arises prenataly and is ussually diagnosed during prenatal sonographic screening investigation or just in neonatal period. Ethiopathogenic factors of the disease are not well known and clinical features are various. Prenataly, congenital disease can be presented as cardiac failure or fetal hydrops. Postnatal clinical picture is usually asymptomatic and vascular anomaly is found during screening sonographic investigation of the brain or it is manifested as cardiac insufficiency in varying degrees. An important part of patient management is a multidisciplinary approach that allows early diagnosis of the disease, which is a prerequisite for successful treatment.
Authors present two case reports of newborns with different clinical manifestation and management in early postnatal period.
Key words:
newborn, vascular anomaly, vein of Galen
Sources
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Labels
Neonatology Paediatrics General practitioner for children and adolescentsArticle was published in
Czech-Slovak Pediatrics
2016 Issue 5-6
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