Vein of Galen aneurysmal malformation

Czech version

Authors: A. Kubátová ¹; R. Pádr ²
Authors‘ workplace: Novorozenecké oddělení s JIRP, Gynekologicko-porodnická klinika 2. LF UK a FN Motol, Praha ¹; Klinika zobrazovacích metod 2. LF UK a FN Motol, Praha ²
Published in: Čes-slov Neonat 2024; 30 (1): 37-45.
Category: Reviews

Overview

Vein of Galen aneurysmal malformation is a rare life threatening congenital malformation of cerebral vessels. Size and type of malformation has a major influence on clinical manifestations especially on hemodynamics. In the neonatal period the most common type is choroidal which causes heart failure in the newborn shortly after birth or even prenatally. Patients need multidisciplinary approach. Causal therapy belongs to the hands of interventional radiologists. Thanks to these methods and highly specialized care in neonatal intensive care units the mortality of these patients is no longer 100% as in the 20th century. Nevertheless, it is still a disease with high mortality and morbidity. The article is supplemented with a short overview of our patients from the last 12 years.

Keywords:

Neonates – embolization – heart failure – malformation of vena magna Galeni

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Konflikt zájmu: žádný Došlo do redakce: 28. 2. 2024

Adresa pro korespondenci:
MUDr. Aneta Kubátová
Novorozenecké oddělení s JIRP
Gynekologicko-porodnická klinika 2. LF UK a FN Motol
V Úvalu 84
150 06 Praha 5
email: aneta.kubatova@fnmotol.cz