Microscopic polyangiitis

Czech version

Authors: Daniel Tobiáš; Kristína Brázdilová; Zdenko Killinger; Juraj Payer
Authors‘ workplace: V. interná klinika LF UK a UN Bratislava, Nemocnica Ružinov, Slovenská republika
Published in: Vnitř Lék 2020; 66(4): 249-252
Category: Case Report

Overview

Microscopic polyangiitis is a rare, systemic, necrotizing, pauci-immune, ANCA associated small vessel vasculitis, with no evidence of granulomatous inflammation. Diagnosing microscopic polyangiitis is often difficult because of it´s presentation by a number of non-specific symptoms. We treated a 35-year old patient, who was admitted for migrating arthritis and fever with papulous rash. In this case, we want to point out the importance of considering the diagnosis of MPA and similar rare diseases in the process of differential diagnosis, mainly in patients presenting with non-specific symptoms, because the mortality of this disease without adequate treatment is alarmingly high.

Keywords:

vasculitis – Pancreatitis – ANCA – glomerulonephritis – cerebritis – polyangiitis

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