Congenital Adrenal Hyperplasia in Adults

Czech version

Authors: Jana Vrbíková
Authors‘ workplace: Endokrinologický ústav, Praha
Published in: Vnitř Lék 2016; 62(Suppl 3): 131-134
Category: Reviews

Overview

Congenital adrenal hyperplasia is a life-long disease requiring an integrated therapy. It may negatively influence the quality of life. In childhood, the main problems of the care of these patients involve sex determination and ensuring optimum growth and puberty. The therapeutic goals for adults are the prevention of Addisonian crisis and ensuring the best possible quality of life, including fertility.

Key words:
androgens – cardiovascular risk – congenital adrenal hyperplasia – bone density – testicular rest tumors

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