Desmoid fibromatosis – a rare mesenteric tumor

Czech version

Authors: Grochol L. ¹; Cibulková I. ¹; Hrudka J. ²; Hajer J. ¹
Authors‘ workplace: Divize gastroenterologie a hepatologie, Interní klinika 3. LF UK a FN Královské Vinohrady, Praha ¹; Ústav patologie 3. LF UK a FN Královské Vinohrady, Praha ²
Published in: Gastroent Hepatol 2022; 76(1): 67-71
Category:
doi: https://doi.org/10.48095/ccgh202267

Overview

In the following report, we present the case of a 31-year-old patient examined for a suspected small bowel tumour. Small bowel tumours are relatively rare and definitive diagnosis is often preceded by surgical resection. The same was true for our patient examined for a soft tissue lesion found with imaging techniques in close proximity to the small intestine. After ruling out hormonal activity, diagnostic laparotomy was performed. Desmoid fibromatosis, a rare tumour of the mesentery, was confirmed histopathologically. Although without metastatic potential, desmoid fibromatosis is a tumour with moderately malignant potential for aggressive growth into surrounding structures and organs and a large percentage of local recurrences.

Keywords:

desmoid fibromatosis – small intestine tumours – mesentery – sarcoma

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