Congenital pulmonary airway malformation
Authors:
J. Micherová 1; P. Rejtar 2; B. Frýbová 3; Hubert Vaníček 1
Authors‘ workplace:
Dětská klinika LF a FN Hradec Králové
1; Radiologická klinika LF a FN Hradec Králové
2; Klinika dětské chirurgie 2. LF UK a FN Motol, Praha
3
Published in:
Čes-slov Pediat 2021; 76 (5): 240-245.
Category:
Original Papers
Overview
Congenital pulmonary airway malformation (CPAM) with its incidence 1:25–35 000 belongs to the most frequent congenital lung anomalies. Pulmonary sequestration (PS) occures less often. These malformations can be mixed sometimes, called hybrid lesions. They need to be correctly diagnosed in patients with unknown pulmonary lesions of any age. They can be easily diagnosed prenatally by ultrasonography. Clinical presentation differs from asymptomatic lesions to respiratory failure of child. Therapeutic approach depends on symptomps, size and type of the malformation as well as personal experience.
Keywords:
congenital pulmonary airway malformation – CPAM – congenital cystic adenomatoid malformation – CCAM – congenital thoracic malformation – CTM – congenital lung masses – CLM – bronchopulmonary sequestration – PS
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Labels
Neonatology Paediatrics General practitioner for children and adolescentsArticle was published in
Czech-Slovak Pediatrics
2021 Issue 5
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