Pneumothorax in a Girl with Marfan's Syndrome

Czech version

Authors: J. Varvařovská; V. Vyskočil; K. Pizingerová; Sýkora J. Stožický F.; Z. Chudáček; V. Špidlen
Authors‘ workplace: Dětská klinika FN a LF UK, Plzeň, přednosta doc. MUDr. F. Stožický, DrSc. Ortopedická klinika FN a LF UK, P1zeň, 2 přednosta doc. MUDr. K. Koudela, CSc Radiodiagnostické oddělení Bory, Fakultní nemocnice, Plzeň, 3 prim. MUDr. Z. Chudáček, PhD. Chirurgická
Published in: Čes-slov Pediat 2002; (5): 255-258.
Category:

Overview

The authors Present a tase report of a girl suffering from repeated bilateral Pneumothorax due to emphysematous bullae of the uPPer Puhnonary fields. It was necessary to carry out the resection of the heads of uPPer Puhnonary lobes and bilateral Pleurodesis. The Period of convalescence was the time when different examinations esere comPleted with the aim to discover the cause of repeated Pneumothorax. Typical habitus and further signs of connective tissue alterations gave evidence of Marfan Syndrome when 4 Percent of affected Patients have apical bullae with development of repeated Pneumothorax.

Key words:
Marfan Syndrome, Pneumothorax

Full text is not available online.

If interested in a scan of this journal, contact NTO ČLS JEP.