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Mastocytosis in Children


Authors: H. Bučková 1;  J. Feit 2
Authors‘ workplace: Kožní oddělení Pediatrické kliniky FN Brno a LF MU v Brně 1;  Ústav patologie FN Brno a LF MU v Brně 2
Published in: Čes-slov Derm, 85, 2010, No. 3, p. 129-138
Category: Reviews

Overview

Increased number of mastocytes in the skin and/or other tissues and organs is the typical feature of mastocytosis. In children, skin forms of mastocytosis prevail and, usually, heal without therapy. Systemic mastocytosis is rare in children. We discuss WHO classification of mastocytoses and screening protocol, which helps to establish the diagnosis and choose the appropriate therapy and follow-up of affected children.

Key words:
mastocytosis – etiopathogenesis – classification – examination protocol – therapy – differential diagnostics


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