Ňaršanská A., Třeška V., Mírka H., Mukenšnabl P., Chlumská A.: Caroli Disease – Dilatation of Intrahepatic Bile Ducts
Authors:
A. Ňaršanská; V. Třeška; H. Mírka 1; P. Mukenšnabl 2; A. Chlumská 2
Authors‘ workplace:
Chirurgická klinika FN a LF UK v Plzni, přednosta: prof. MUDr. Vladislav Třeška, DrSc.
; Radiodiagnostická klinika FN a LF UK v Plzni, přednosta: doc. MUDr. Boris Kreuzberg, CSc.
1; Šiklův patologicko-anatomický ústav FN a LF UK v Plzni, přednosta: prof. MUDr. Michal Michal, Ph. D.
2
Published in:
Rozhl. Chir., 2011, roč. 90, č. 5, s. 281-284.
Category:
Monothematic special - Original
Overview
Caroli disease is a rare congenital condition characterized by a non-obstructive saccular or fusiform multi-focal segmental dilatation of the intrahepatic bile ducts and the frequent formation of the intrahepatic calculi. It can affect the entire liver with manifestations in the childhood, or only some segments, which may be an asymptomatic condition found accidentally in the adulthood. In other cases, the condition is manifested primarily with tract infections. The authors of the three case reports describe pitafalls of the diagnosis and treatment of the segmental Caroli disease, which is manifested in the adulthood. The treatment was a resection of the affected liver segments.
Key words:
Caroli disease – dilatation of the intrahepatic bile – surgery treatment
Sources
1. Chlumská, A. Kongenitální cystická dilatace intrahepatálních žlučovodů (Caroliho nemoc). Čas. Lék. čes., 129, 1990, č. 6, s. 184–187.
2. Brodanová, M., a spol. Onemocnění žlučníku a žlučových cest. Praha: Grada Publishing, 1998.
3. Hermann, J., Procházka, V., Schneidera, P. Diferenciální diagnostika ikteru. Postgrad. Med., 2001, 3, s. 912–926.
4. Scherlock, S., Doplet, J. Diseases of the Liver and Biliary System. 10th ed, Oxford: Blackwell Science, 1997.
5. Ashish, K. G., Aradhana, G., Bhardwaj, V. K., Chansoria, M. Caroli’s Disease, Indian J. Pediatr., 2006; 73 (3): 233–235.
6. Shorbagi, A., Bayeaktar, Y. Experience of a single center with congenital hepatic fibrosis: a review of the literature. World J. Gastroenterol., 2010 Feb 1414; 16(6): 683–690.
7. Totkas, S., Hohenberger, P. Cholangiocellular carcinoma associated with segmental Caroli disease. Eur. J. Surg. Oncol., 2000; 26: 520–521.
8. Ulrich, F., Pratschke, J., Pascher, A., Neumann, U. P., Lopez-Hänninen, E., Jonas, S., Neuhaus, P. Long-term outcome of liver resection and transplantation for Caroli disease and syndrome. Ann. Surg., 2008 Feb; 247(2): 357–364.
9. Habib, S., Shakil, O., Couto, O. F., Demetris, A. J., Fung, J. J., Marcos, A., Chopra, K. Caroli disease and orthotopic liver transplantation. Liver Transpl., 2006 Mar; 12(3): 416–421.
10. Bockhorn, M., Malagó, M., Lang, H., Nadalin, S., Paul, A., Saner, F., Frilling, A., Broelsch, C. E. The role of surgery in Caroli disease. J. Am. Coll. Surg., 2006 Jun; 202(6): 928–932. Epub 2006 Apr 21.
Labels
Surgery Orthopaedics Trauma surgeryArticle was published in
Perspectives in Surgery
2011 Issue 5
Most read in this issue
- Šmíd D., Novák P., Liška V., Třeška V.: Pilonidal Sinus – Surgical Management at Our Surgical Clinic
- Ňaršanská A., Třeška V., Mírka H., Mukenšnabl P., Chlumská A.: Caroli Disease – Dilatation of Intrahepatic Bile Ducts
- Hrabálek L., Starý M., Rosík S., Wanek T.: Surgery for Symptomatic Vertebral Hemangiomas
- Šafránek J., Špidlen V., Vodička J.: Mediastinal Cysts, Surgical Management