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Weber-Christian disease: a case report


Authors: Kristína Brázdilová 1;  Daniel Čierny 1;  Katarína Hrubišková 1;  Lukáš Plank 2;  Zdenko Killinger 1;  Juraj Payer 1
Authors‘ workplace: V. interná klinika LF UK a UNB, Nemocnica Ružinov, Bratislava, Slovenská republika 1;  Ústav patologickej anatómie JLF UK a UNM, Martin, Slovenská republika 2
Published in: Vnitř Lék 2018; 64(10): 961-965
Category: Case Report

Overview

Weber-Christian disease is a rare disease from the group of chronic fibrosing conditions characterized by inflamma­tion of the adipose tissue – panniculitis and fibrosing with frequent systemic manifestations. Etiopathogenesis of the disease is not fully known, participation of autoimmune mechanisms is anticipated. Here, we report a case of a patient with this rare disease, diagnosed after a long and demanding diagnostic process, including repeated lapa­rotomies. However, after immunosuppressive therapy, clinical and laboratory symptomatology improved rapidly as well as the patient’s quality of life.

Key words:

panniculitis – sclerosing mesenteritis – Weber-Christian disease


Sources
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Diabetology Endocrinology Internal medicine
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