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Congenital Dermatofibrosarcoma Protuberans


Authors: Z. Plzáková 1;  M. Důra 1,2;  P. Dundr 1,2;  J. Štork 1
Authors‘ workplace: Dermatovenerologická klinika 1. LF UK a VFN, Praha přednosta prof. MUDr. J. Štork, CSc. 1;  Ústav patologie 1. LF UK a VFN, Praha přednosta doc. MUDr. P. Dundr, Ph. D. 2
Published in: Čes-slov Derm, 91, 2016, No. 1, p. 18-21
Category: Case interpretation

Overview

Dermatofibrosarcoma protuberans is a slowly growing skin tumor of low malignant potential and high local recurrence rate. It appears in adults, infantile and congenital forms are rare and their diagnosis is often delayed. We present a case of 32-year-old female with congenital tumour and discuss its differential diagnosis and therapeutic possibilities.

Key words:
dermatofibrosarcoma protuberans – congenital dermatofibrosarcoma protuberans – differential diagnosis – wide local excision – imatinib mesylate


Sources

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Labels
Dermatology & STDs Paediatric dermatology & STDs
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