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Epidermolysis Bullosa Acquisita with Ocular Complications


Authors: L. Drlík 1;  L. Pock 2;  J. Krtička 3
Authors‘ workplace: Dermatovenerologické oddělení, Šumperská nemocnice, a. s. přednosta prim. MUDr. Lubomír Drlík 1;  Dermatohistopatologická laboratoř, Praha vedoucí doc. MUDr. Lumír Pock, CSc. 2;  Oční ambulance, Zábřeh na Moravě vedoucí MUDr. Jakub Krtička 3
Published in: Čes-slov Derm, 89, 2014, No. 1, p. 16-21
Category: Case Reports

Overview

The authors present a case of a patient with epidermolysis bullosa acquisita and Crohn’s disease. The patient has been treated for 13 years with combined immunosuppressive and corticosteroid therapy with only limited morbostatic effect. Initially, classic form dominated in the clinical picture. Later, a bullous pemphigoid-like and a Brunsting-Perry pemphigoid-like lesions occurred, as well as a significant eye involvement.

Key words:
subepidermal blisters – epidermolysis bullosa acquisita – Crohn’s disease – anti-type VII collagen antibodies


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