Consensual guidelines of the Czech National Haemophilia Programme (CNHP) for factor replacement therapy in patients with haemophilia during invasive procedures and surgery
Authors:
R. Hrdličková 1; P. Smejkal 2; J. Blatný 3; A. Hluší 4; V. Komrska 5; M. Penka 2; J. Šlechtová 6; J. Blatný 3; B. Blažek 7; Z. Čermáková 1; Z. Černá 8; P. Ďulíček 9; J. Hak 10; A. Hluší 4; R. Hrdličková 1; V. Komrska 5; P. Ovesná 11; D. Pospíšilová 12; D. Procházková 13; P. Smejkal 2; J. Šlechtová 6; P. Timr 14; J. Ullrychová 15; I. Vonke 16; L. Walterová 17; M. Penka 2
Authors‘ workplace:
Krevní centrum a Klinika hematoonkologie, Fakultní nemocnice Ostrava
1; Oddělení klinické hematologie, Fakultní nemocnice Brno
2; Oddělení dětské hematologie, Fakultní nemocnice Brno
3; Hemato-onkologická klinika, Fakultní nemocnice Olomouc
4; Klinika dětské hematologie a onkologie, Fakultní nemocnice v Motole, Praha
5; Ústav klinické biochemie a hematologie, Fakultní nemocnice Plzeň
6; Klinika dětského lékařství, Fakultní nemocnice Ostrava
7; Dětská klinika, Fakultní nemocnice Plzeň
8; IV. Interní hematologická klinika, Fakultní nemocnice Hradec Králové
9; Dětská klinika, Fakultní nemocnice Hradec Králové
10; Institut biostatistiky a analýz Lékařské fakulty, Masarykova univerzita, Brno
11; Dětská klinika, Fakultní nemocnice Olomouc
12; Dětská klinika, Krajská zdravotní a. s., Masarykova nemocnice v Ústí nad Labem
13; Dětské oddělení, Nemocnice České Budějovice
14; Oddělení klinické hematologie, Krajská zdravotní a. s., Masarykova nemocnice v Ústí nad Labem
15; Oddělení klinické hematologie, Nemocnice České Budějovice
16; Oddělení klinické hematologie, Krajská nemocnice Liberec
17
Published in:
Transfuze Hematol. dnes,22, 2016, No. 1, p. 39-43.
Category:
Comprehensive Reports, Original Papers, Case Reports
Pozn:
*Pracovní skupina ČNHP pro standardy
**Jménem Koordinační rady a Výkonné rady ČNHP
Overview
Haemophilia A and B are rare congenital bleeding disorders. Invasive procedures and surgery can be performed safely in patients with haemophilia without inhibitors due to the availability of coagulation factors VIII and IX. The aim of these guidelines is to summarize treatment experience and recommendations including optimal factor VIII/IX levels for surgical procedures and replacement therapy duration following these.
KEY WORDS:
haemophilia – surgery – factor VIII – factor IX – replacement treatment
Sources
1. Guidelines for the Management of Hemophilia. World Federation of Hemophilia 2012. Dostupné na www: http://www1.wfh.org/publication/files/pdf-1472.pdf
2. Australian Haemophilia Centre Directors´ Organisation (AHCDO). Guideline for the management of patients with haemophilia undergoing surgical procedures. November 2010. Dostupné na www: http://www.ahcdo.org.au/sitebuilder/publications/knowledge/asset/files/10/surgery guidelinesfinal2010.pdf
3. Bátorová A, Jankovičová D, Žarnovičanová M, et al. Národné štandardné postupy pre liečbu hemofilie a iných vrodených koagulopatií v Slovenskej republike. Lek Obz 2008; 56: 330–340.
4. Hermans C, Altisent C, Batorova A, et al. Replacement therapy for invasive procedures in patients with haemophilia: literature review, European survey and recommendation. Haemophilia 2009; 15: 639–658.
5. Ljung RC, Knobe K. How to manage invasive procedures in children with haemophilia. Br J Haematol 2012; 157: 519–528.
6. Wallny TA, Strauss AC, Goldmann G, et al. Elective total knee arthroplasty in haemophilic patients. Proposal for a clinical pathway. Hamostaseologie 2014; 34(Suppl 1): S23–29.
7. Wiedel J, Stabler S, Geraghty S, Funk S. Joint replacement surgery in hemophilia. World Federation of Hemophilia 2010. Dostupné na www: http://www1.wfh.org/publication/files/pdf-1210.pdf
8. Teitel JM, Carcao M, Lillicrap D, et al. Orhopaedic surgery in haemophilia patients with inhibitor: a practical guide to haemostatic surgical and rehabilitative care. Haemophilia 2009; 15: 227–239.
9. Batorova A, Holme P, Gringeri A, et al. Continuous infusion in haemophilia: current practice in Europe. Haemophilia 2012; 18(5): 753–759.
10. Australian Haemophilia Centre Directors’Organisation (AHCDO). A consensus statement on the dental treatment of patients with inherited bleeding disorders July 2010. Dostupné na www: http://www.ahcdo.org.au/sitebuilder/publications/knowledge/asset/files/16/dentalguidelinesforwebsitedec10.pdf
11. Anderson JAM, Brewer A, Creagh D, et al. Guidance on the dental management of patients with haemophilia and congenital bleeding disorders. Br Dent J 2013; 215: 497–504.
12. Ozelo MC. Surgery in patients with hemophilia: is thromboprophylaxis mandatory? Thromb Res 2012; 130(Suppl 1): S23–S26.
13. Zakarija A, Aledort L. How we treat: venous trombembolism prevention in haemophilia patients undergoing major orthopaedics surgery. Haemophilia 2009; 15: 1337–1338.
14. Hermans C. Venous thromboembolic disease in patients with haemophilia. Thromb Res 2012; 130(Suppl 1): S50–S52.
15. Tintillier V, Branche J, Maunoury V, et al. Colonoscopy in patients with haemophilia: the duration of factor coverage must be adjusted to suit the procedure. Haemophilia 2013; 19: e296–e323.
16. Fogarty PF, Koudide P. How we manage prostate biopsy and prostate cancer therapy in men with haemophilia. Haemophilia 2012; 18: e88–e90.
Labels
Haematology Internal medicine Clinical oncologyArticle was published in
Transfusion and Haematology Today
2016 Issue 1
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