#PAGE_PARAMS# #ADS_HEAD_SCRIPTS# #MICRODATA#

Vertigo with sudden hearing loss and eye symptoms – Cogan‘s syndrome


Authors: F. Campsie;  Richard Salzman;  J. Heřman
Authors‘ workplace: Klinika otorinolaryngologie a chirurgie hlavy a krku LF UP a FN Olomouc
Published in: Otorinolaryngol Foniatr, 72, 2023, No. 4, pp. 221-226.
Category: Case Reports
doi: https://doi.org/10.48095/ccorl2023221

Overview

Cogan’s syndrome is a rare systemic autoimmune vasculitis affecting mostly young adults. This case report describes a young female patient with typical symptoms of interstitial keratitis and vertigo with sudden sensorineural hearing loss resembling Ménièr’s disease. The role of otoneurological and audiometry examinations is discussed in relationship with the course of systemic treatment in cooperation with a rheumatologist. The aim of this article is to raise awareness of Cogan’s syndrome in order to include it to the differential diagnosis of paroxysmal vertigo with sudden sensorineural hearing loss.

Keywords:

autoimmune disease – Cogan‘s syndrome – sudden hearing loss – vestibular impairment – keratitis


Sources

1. Haynes BF, Kaiser-Kupfer MI, Mason P et al. Cogan syndrome: studies in thirteen patients, long-term follow-up, and a review of the literature. Medicine (Baltimore) 1980; 59 (6): 426–441.

2. Grasland A, Pouchot J, Hachulla E et al. Typical and atypical Cogan‘s syndrome: 32 cases and review of the literature. Rheumatology (Oxford) 2004; 43 (8): 1007–1015. Doi: 10.1093/rheumatology/keh228.

3. Kundell SP, Ochs HD. Cogan syndrome in childhood. J Pediatr 1980; 97 (1): 96–98. Doi: 10.1016/s0022-3476 (80) 80142-9.

4. D‘Aguanno V, Ralli M, de Vincentiis M et al. Optimal management of Cogan‘s syndrome: a multidisciplinary approach. J Multidiscip Healthc 2018; 11: 1–11. Doi: 10.2147/JMDH.S150940.

5. Morovic Vergles J, Radic M, Kovacic J et al. Successful use of adalimumab for treating rheumatoid arthritis with autoimmune sensorineural hearing loss: two birds with one stone. J Rheumatol 2010; 37 (5): 1080–1081. Doi: 10.3899/jrheum.091342.

6. Mora P, Calzetti G, Ghirardini S et al. Cogan‘s syndrome: State of the art of systemic immunosuppressive treatment in adult and pediatric patients. Autoimmun Rev 2017; 16 (4): 385–390. Doi: 10.1016/j.autrev.2017.02.009.

7. Cundiff J, Kansal S, Kumar A et al. Cogan‘s syndrome: a cause of progressive hearing deafness. Am J Otolaryngol 2006; 27 (1): 68–70. Doi: 10.1016/j.amjoto.2005.07.006.

8. Gluth MB, Baratz KH, Matteson EL et al. Cogan syndrome: a retrospective review of 60 patients throughout a half century. Mayo Clin Proc 2006; 81 (4): 483–488. Doi: 10.4065/81.4.483.

9. Cochrane AD, Tatoulis J. Cogan‘s syndrome with aortitis, aortic regurgitation, and aortic arch vessel stenoses. Ann Thorac Surg 1991; 52 (5): 1166–1167. Doi: 10.1016/0003-4975 (91) 91304-e.

10. Peters BR, Wyss J, Manrique M. Worldwide trends in bilateral cochlear implantation. Laryngoscope 2010; 120 (Suppl 2): S17–44. Doi: 10.1002/lary.20859.

11. Wang JR, Yuen HW, Shipp DB et al. Cochlear implantation in patients with autoimmune inner ear disease including cogan syndrome: a comparison with age- and sex-matched controls. Laryngoscope 2010; 120 (12): 2478–2483. Doi: 10.1002/lary.21060.

Labels
Audiology Paediatric ENT ENT (Otorhinolaryngology)

Article was published in

Otorhinolaryngology and Phoniatrics

Issue 4

2023 Issue 4

Most read in this issue
Topics Journals
Login
Forgotten password

Enter the email address that you registered with. We will send you instructions on how to set a new password.

Login

Don‘t have an account?  Create new account

#ADS_BOTTOM_SCRIPTS#