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Case report of a gigantic recurrent angiomyolipoma in a horseshoe kidney


Authors: Markéta Hulová;  Michal Staník;  Daniel Macík;  Jan Doležel
Authors‘ workplace: Oddělení urologické onkologie, Masarykův onkologický ústav, Brno
Published in: Ces Urol 2020; 24(1): 69-73
Category: Case report

Prezentujeme kazuistiku objemného recidivujícího angiomyolipomu podkovovité ledviny u mladé pacientky s podezřením na syndrom tuberózní sklerózy. Stav byl řešen opakovanou cytoredukční operací v kombinaci se systémovou léčbou mTOR inhibitory.

Overview

We present a case report of gigantic recurrent angiomyolipoma of the horseshoe kidney in a young patient with suspected tuberous sclerosis syndrome. The condition was solved by repeated cytoreductive surgery in combination of systemic treatment with mTOR inhibitors.

Keywords:

angiomyolipoma – tuberous sclerosis – horseshoe kidney – mTOR inhibitor


Sources

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Labels
Paediatric urologist Nephrology Urology Clinical oncology
Topics Journals
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